Anomalous Origin of the Left Coronary Artery from the Pulmonary Artery in Alagille Syndrome

作者：Lemoine Tara J^*; Kaza Aditya K; Gray Robert; Day Ronald W; Tani Lloyd Y; Poss William Bradley

来源：Congenital Heart Disease, 2010, 5(5): 462-464.

DOI：10.1111/j.1747-0803.2010.00386.x

• ALCAPA
• Alagille Syndrome
• Mitral Valve

Alagille syndrome is a dominantly inherited multisystem disorder involving multiple organs including the liver, heart, eyes, face, and skeleton. Congenital heart defects, the majority of which are right-sided, contribute significantly to the mortality of these patients. We report a patient with Alagille syndrome who presented with mitral valve regurgitation requiring valvuloplasty and subsequent mitral valve replacement. The patient was ultimately diagnosed with anomalous origin of the left coronary artery from the pulmonary artery and underwent successful reimplantation.

• 出版日期2010-10