Multidisciplinary Management of Mastocytosis: Nordic Expert Group Consensus

作者：Broe**y Olsen Sigurd^*; Dybedal Ingunn; Gulen Theo; Kristensen Thomas K; Moller Michael B; Ackermann Leena; Saaf Maria; Karlsson Maria; Agertoft Lone; Brixen Kim; Hermann Pernille; Stylianou Eva; Mortz Charlotte G; Torfing Trine; Havelund Troels; Sander Birgitta; Bergstrom Anna; Bendix Marie; Garvey Lene H; Weis Bjerrum Ole; Valent Peter; Bindslev Jensen Carsten; Nilsson Gunnar; Vestergaard Hanne; Hagglund Hans

来源：Acta Dermato-Venereologica, 2016, 96(5): 602-+.

DOI：10.2340/00015555-2325

• mastocytosis
• systemic mastocytosis
• urticaria pigmentosa
• classification
• diagnostic criteria
• mast cell
• multidisciplinary management

Mastocytosis is a heterogeneous group of diseases defined by an increased number and accumulation of mast cells, and often also by signs and symptoms of mast cell activation. Disease subtypes range from indolent to rare aggressive forms. Mastocytosis affects people of all ages and has been considered rare; however, it is probably underdiagnosed with potential severe implications. Diagnosis can be challenging and symptoms may be complex and involve multiple organ-systems. In general it is advised that patients should be referred to centres with experience in the disease offering an individualized, multidisciplinary approach. We present here consensus recommendations from a Nordic expert group for the diagnosis and general management of patients with mastocytosis.

• 出版日期2016-7