Decreasing Activity and Altered Protein Processing of Human Iduronate-2-sulfatase Mutations Demonstrated by Expression in COS7 Cells

作者:Charoenwattanasatien Ratana; Cairns James R Ketudat; Keeratichamroen Siri****; Sawangareetrakul Phannee; Tanpaiboon Pranoot; Wattanasirichaigoon Duangrurdee; Pangkanon Suthipong; Svasti Jisnuson; Champattanachai Voraratt*
来源:Biochemical Genetics, 2012, 50(11-12): 990-997.
DOI:10.1007/s10528-012-9538-9