Alveolar soft part sarcoma of the oral and maxillofacial region: clinical analysis in a series of 18 patients

作者:Wang, Hong-Wei; Qin, Xing-Jun*; Yang, Wen-Jun; Xu, Li-Qun; Ji, Tong; Zhang, Chen-Ping
来源:Oral Surgery Oral Medicine Oral Pathology Oral Radiology, 2015, 119(4): 396-401.
DOI:10.1016/j.oooo.2014.12.013

摘要

Objectives. To summarize the clinical features, diagnosis, treatment strategies, and prognosis of alveolar soft part sarcoma (ASPS) of the oral and maxillofacial region. @@@ Study design. We performed a retrospective study in a consecutive series of 18 patients with ASPS of the oral and maxillofacial region between 1995 and 2013. Demographic characteristics, tumor sizes, sites, tumor metastasis, diagnosis, treatments, and overall follow-ups were documented. @@@ Results. The 18 patients were diagnosed pathologically with primary tumor developed on the tongue (10), the cheek (5), the pharynx (1), and the gingiva (2) with an average tumor size of 4 cm. At the latest follow-up, 1 patient with lung metastases survived for 23 months; 1 died 3 months after the confirmation of local recurrence and multiple pulmonary metastases; the rest of the patients were disease free and remained in good health. @@@ Conclusions. ASPS of the oral and maxillofacial region appears to have special clinical characteristics.