A variant of Poland syndrome associated with dextroposition

作者:Mutlu Hakan*; Sildiroglu Onur; Basekim Cinar C; Kizilkaya Esref
来源:Journal of Thoracic Imaging, 2007, 22(4): 341-342.

摘要

Poland syndrome is characterized by partial or complete absence,of pectorahs muscles, ipsilateral syndactyly, and occasionally other malformations of the anterior chest wall and breast. Other associated anomalies including dextrocardia, renal malformations, and vertebral anomalies, have been reported in rare cases. The condition is more frequent among males, and usually, occurs on the right hemithorax in the unilateral form. The syndrome is believed to be caused by a genetic disorder,that reduces the embryonal circulation in the subclavian and Vertebral arteries. We report a 20-year-old man with Poland syndrome on the left hemithorax; which is rarely associated wiih dextroposition.

  • 出版日期2007-11
  • 单位中国人民解放军军事医学科学院