Maffucci Syndrome and Intracranial Chondrosarcomas: A Case Report Featuring Spontaneous Resolution of Sixth Nerve Palsy

作者:Munro Monique; Costello Fiona; Burrowes David; Yau Ryan*
来源:Journal of Neuro-Ophthalmology, 2015, 35(1): 41-44.
DOI:10.1097/WNO.0000000000000151

摘要

Maffucci syndrome is a rare disease process characterized by enchondromatosis with cutaneous hemangiomatosis. We report a 20-year-old woman with Maffucci syndrome with a 5-day history of diplopia. She was found to have a left sixth nerve palsy due to a parasellar chondrosarcoma. Three weeks later, the patient's diplopia spontaneously resolved. This unusual clinical course prompted us to review frequency of sixth nerve palsy with skull base neoplasms and the phenomenon of spontaneous resolution of diplopia.

  • 出版日期2015-3