A case of non-functioning huge adrenocortical carcinoma extending into inferior vena cava and right atrium

作者：Kim Kye Hun; Park Jong Chun^*; Lim Sang Yup; Sohn Il Suk; Yun Kyung Ho; Cho Sang Hee; Hong Young Joon; Park Hyung Wook; Kim Ju Han; Kim Weon; Ahn Young Keun; Chung lk Joo; Jeong Myung Ho; Cho Jeong Gwan; Kang Jung Chaee

来源：Journal of Korean Medical Science, 2006, 21(3): 572-576.

DOI：10.3346/jkms.2006.21.3.572

• adrenocortical carcinoma
• neoplasm metastasis
• vena cava
• inferior

Primary adrenocortical carcinoma (ACC) is a rare tumor and its usual sites of metastasis are the lung (71%), lymph node (68%), liver (42%), and bone (26%). However, intracaval invasion extending into the right atrium is very rare and spontaneous regression of tumor burden in adrenal carcinoma is also rare. We report a case of ;ACC with direct invasion of the inferior vena cava and right atrium. A 34-yr-old male patient presented with progressive dyspnea, weight loss, and poor oral intake over 3 months. Non-functioning ACC with direct invasion of the inferior vena cava and right atrium was confirmed by imaging, pathologic, and hormonal study. Chemo-radiotherapy was attempted. However, tumor burden was not changed, but rather toxic hepatitis and thrombocytopenia were developed. His subjective symptoms and general conditions were improved after 1 month of conservative management and the patient was discharged. During clinical follow-up, this tumor showed spontaneous regression.

• 出版日期2006-6
• 单位河北医科大学