Aorto-Tracheopexy in the Treatment of Hunter Syndrome

作者：Quong Whitney L; Kanani Mazyar; Elliott Martin J^*

来源：Annals of Thoracic Surgery, 2015, 99(6): 2190-2192.

DOI：10.1016/j.athoracsur.2014.08.048

Hunter syndrome is a multisystem genetic disease in which a significant proportion of morbidity and mortality arise from respiratory dysfunction. Notably, tracheal abnormalities in Hunter syndrome can compromise clinical stability, and management is primarily supportive. We describe here the first successful implementation of aorto-tracheopexy in a 19-year-old patient as a surgical strategy to resolve progressive respiratory deterioration.

• 出版日期2015-6