A prospective study of the presentation and management of dancing eye syndrome/opsoclonus-myoclonus syndrome in the United Kingdom

作者：Pang K Ki; de Sousa Carlos; Lang Bethan; Pike Michael G^*

来源：European Journal of Paediatric Neurology, 2010, 14(2): 156-161.

DOI：10.1016/j.ejpn.2009.03.002

• Dancing Eye Syndrome
• Opsoclonus-Myoclonus syndrome
• Prospective Study

The incidence, mode of presentation and management of Dancing Eye Syndrome/Opsoclonus-Myoclonus Syndrome (DES/OMS) was prospectively evaluated in 20 United Kingdom (UK) paediatric neurology centres by questionnaire over a 24-month period between 2003 and 2005
Nineteen children were notified, giving an incidence of 0 18 cases per million total population per year Mean age at presentation was 18 months (range 3-42 months) Fifteen families consented to participate in the study Atypical features were present in 6/15 cases including very delayed presentation of opsoclonus, dysphagia, and rapid spontaneous improvement without treatment
Only 4/15 cases were associated with ne

• 出版日期2010-3