Airway stenting in a child with spondyloepiphyseal dysplasia congenita: 13-Year survival

作者:Nenna Raffaella*; Midulla Fabio; Masi Laura; Bacci Giacomo Maria; Frassanito Antonella; Baggi Roberto; Brandi Maria Luisa; Avenali Stefano; Mirabile Lorenzo; Serio Paola
来源:International Journal of Pediatric Otorhinolaryngology, 2017, 99: 13-16.
DOI:10.1016/j.ijporl.2017.05.008

摘要

We describe the case of a boy with spondyloepiphyseal dysplasia congenita. At birth, he experienced severe respiratory distress necessitating tracheotomy. Endoscopy done because mechanical ventilation failed to resolve desaturations disclosed severe tracheo-bronchomalacia. A Polyflex silicone stent was placed in the trachea (replaced by Y-Dumon stent) and 2 Palmaz metallic stents in the mainstem bronchi (overlapped with 2 Jomed stents 5 years later). Airway stenting guaranteed a suitable respiratory status and allowed a child who was expected to die at birth, to reach 13.5 years old in good conditions.

  • 出版日期2017-8

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