Adult Langerhans cell histiocytosis and sclerosing cholangitis: a case report and review of the literature

作者:Hatemi Ibrahim*; Baysal Birol; Senturk Hakan; Behzatoglu Kemal; Bozkurt Erol Rustu; Ozbay Gulsen
来源:Hepatology International, 2010, 4(3): 653-658.
DOI:10.1007/s12072-010-9205-3

摘要

Sclerosing cholangitis is a rare complication of Langerhans cell histiocytosis in children which can result in liver failure. This combination is even rarer in adults.
We report a 65-year-old female who developed sclerosing cholangitis 4 years after the diagnosis of Langerhans cell histiocytosis.
Sclerosing cholangitis caused by Langerhans cell histiocytosis is a rare condition in the adult population, but it has a high mortality. There is no definitive therapy other than liver transplantation. The long-term efficacy of liver transplantation remains unknown.

  • 出版日期2010-9