Autoimmunity in X-linked agammaglobulinemia: Kawasaki disease and review of the literature

作者：Behniafard Nasrin; Aghamohammadi Asghar^*; Abolhassani Hassan; Pourjabbar Sarvenaz; Sabouni Farah; Rezaei Nima

来源：Expert Review of Clinical Immunology, 2012, 8(2): 155-159.

DOI：10.1586/ECI.11.94

• autoimmunity
• Kawasaki disease
• X-linked agammaglobulinemia

Although autoimmunity phenotype is surprisingly common in patients with different types of primary antibody deficiency, it is much less frequent in X-linked agammaglobulinemia (XLA). Herein, we report on a 15-month-old boy with XLA who also suffered from Kawasaki disease. The current case presentation is the first report of an association between Kawasaki disease and XLA. XLA could be considered as a special opportunity to understand autoimmunity in the near absence of immunoglobulins.

• 出版日期2012-2