A facial inflammatory myofibroblastic tumour in a 6-year-old girl: Plastic surgery lessons from a rare case

作者：Modarressi Ali^*; Pietramaggiori Giorgio; Bezzola Thierry; Lacroix Sylvain; Richter Michel; Rilliet Benedict; Pittet Brigitte

来源：Journal of Cranio-Maxillofacial Surgery, 2011, 39(2): 141-144.

DOI：10.1016/j.jcms.2010.11.015

• Myofibroblastic tumour
• Bone remodelling
• Craniofacial plastic surgery

Inflammatory myofibroblastic tumours (IMT) are rare, challenging lesions with respect to differential diagnosis, biological behaviour and treatment.
We reviewed the literature and report a unique case of a large (9 x 8 x 8 cm) IMT in the nasal region of a 6-year-old girl responsible for important facial deformation.
Following surgical resection, without any craniofacial reconstruction, the dysmorphism regressed spontaneously with a good result at 2 years of follow-up.
To date, this is the largest IMT reported. Surprisingly, after simple excision of the tumour the craniofacial bones and soft tissues regained spontaneously their normal anatomical position only after a few months. The bone plasticity was likely due to the young age of patient and the preservation of periosteum and muscles during the surgical excision. We conclude that a conservative approach may be considered as alternative to reconstructive surgery in particular cases in young subjects.

• 出版日期2011-3