Atypical initial presentation of Takayasu arteritis as isolated supra-valvular aortic stenosis

作者：Kim Do Yeon; Kim Hwan Wook^*

来源：Journal of Cardiothoracic Surgery, 2016, 11(1): 15.

DOI：10.1186/s13019-016-0408-0

• Takayasu arteritis
• Supra-valvular aortic stenosis
• Bentall opearation

Background: Among the vascular involvements of Takayasu arteritis, a supra-valvular aortic stenosis has been reported very rarely. We report a case of surgically corrected, supra-valvular aortic stenosis caused by Takayasu arteritis.
Case presentation: A 32-year-old female was diagnosed with supra-valvular aortic stenosis by transthoracic echocardiography for the evaluation of cardiac murmur with constitutional symptoms. Under the impression of nonfamilial sporadic type of supra-valvular aortic stenosis, surgical correction was performed. However, after 1 year from the operation, we could know the cause of her disease through the findings of computed tomographic aortography that Takayasu arteritis was suspected.
Conclusions: Takayasu arteritis should be considered in adult female patients presenting supra-valvular aortic stenosis with constitutional symptoms, even if no typical features of vascular involvement.

• 出版日期2016-1-19