A very rare cause of peripheral precocious puberty in a girl: ovarian sex cord tumor with annular tubules

作者:Sanchez Zahonero Julia; Ruiz Dominguez Jose A; Sanchez Zahonero Sandra; Lopez Garcia Jose
来源:Archivos Argentinos de Pediatria, 2017, 115(3): E179-E182.
DOI:10.5546/aap.2017.e179

摘要

Sex cord tumor with annular tubules is an extremely uncommon gonadal stromal neoplasm. It represents 0.05-0.6% of all ovarian tumors, according to series. An unusual case is presented in a 6-year-old girl, detected as a result of an isosexual peripheral precocious puberty. The highlight of this case is that no mass attached to the ovary was found, but only a gonadal asymmetry without radiological signs of malignancy. After confirming the presence of tumoral cells by intraoperative biopsy, unilateral salpingo-oophorectomy with ipsilateral para-aortic and pelvic lymphadenectomy was performed. Afterwards, the evolution of the patient was favorable.

  • 出版日期2017-6

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