Abdominal lymphangiomatosis in a 38-year-old female: Case report and literature review

作者：Lin Ruo Yang; Zou Hai; Chen Tan Zhou^*; Wu Wei; Wang Jian Hong; Chen Xiao Lei; Han Qing Xi

来源：World Journal of Gastroenterology, 2014, 20(25): 8320-8324.

DOI：10.3748/wjg.v20.i25.8320

• Lymphangioma
• Abdominal lymphangiomatosis
• Gastrointestinal bleeding
• Diffuse pulmonary lymphangiomatosis
• Gorham's disease

Lymphangioma is an uncommon benign tumor that develops in the lymphatic system. Abdominal lymphangiomatosis is extremely rare in adult patients, and the clinical symptoms of this condition are complicated and atypical. We report a case of abdominal lymphangiomatosis in a 38-year-old female who presented with intestinal bleeding and protein-losing enteropathy, as well as lesions in the lung and bones. A computed tomography scan revealed multiple small cystic lesions without enhancement. Histological examination revealed microscopic cysts were submucosal, with walls composed of thin fibrous tissue, and D2-40 stained highlight the lining of the lymphatic channels by immunohistochemical method. We make a comparison with the cases reported before, and also discuss the diagnose of diffuse pulmonary lymphangiomatosis and Gorham's disease.

• 出版日期2014-7-7
• 单位温州医科大学