Adult presentation of combined unilateral atresia of the right proximal pulmonary artery and left patent ductus arteriosus: Case report and embryological considerations

作者：Deutsch Marcus Andre^*; Thieme Sven F; Hinterseer Martin; Johnson Thorsten R C; Pfosser Achim; Reichart Bruno; Nikolaou Konstantin; Behr Juergen

来源：International Journal of Cardiology, 2010, 141(1): E4-E7.

DOI：10.1016/j.ijcard.2008.11.125

• Adult congenital heart disease
• Great vessel anomalies
• Pulmonary artery
• Pulmonary arterial hypertension
• Imaging

We report on a rare case of combined unilateral atresia of the proximal right pulmonary artery (PA) and left patent ductus arteriosus (PDA). A 46 year-old female patient with known PDA and associated advanced pulmonary arterial hypertension presented with progressive hemoptysis and increasing exertional dyspnea. Computed tomography of the chest proved the presence of the known PDA but surprisingly failed to demonstrate an extrapulmonary proximal right PA. We show the imaging features and discuss the embryological background of this rare congenital cardiovascular malformation.

• 出版日期2010-5-14