A Different Therapeutic Strategy for Severe Tetralogy of Fallot with Origin of the Left Pulmonary Artery from the Ascending Aorta: Stenting of the Right Ventricular Outflow Tract before Complete Repair

作者：Saritas Turkay^*; Erdem Abdullah; Karaci Ali R; Demir Fadli; Celebi Ahmet

来源：Congenital Heart Disease, 2012, 7(3): E1-E5.

DOI：10.1111/j.1747-0803.2011.00542.x

• Stent Implantation
• Hypoplastic Pulmonary Artery
• Abnormal Origin

The origin of pulmonary artery branches (particularly the left pulmonary artery) from the ascending aorta is a rare condition. We detected prominent hypoplasia of the main and right pulmonary arteries in a 3.5-month-old 3.7 kg female infant who had tetralogy of Fallot with origin of the left pulmonary artery in the ascending aorta. In order to ensure the development of the right pulmonary artery, a stent was put in that extended from the right ventricular outflow tract to the right pulmonary artery. During follow-up, after the patient's right pulmonary artery had developed sufficiently, a complete repair surgery was done. It is common practice for patients with abnormal origin of the left pulmonary artery to perform the complete repair using the direct reimplantation technique. However, we think that another possibility is to implant the stent in patients with hypoplastic pulmonary artery and branches in the early stages, wait for a short period of time and perform the complete repair surgery before permanent pulmonary hypertension develops.

• 出版日期2012-6