Auxiliary Partial Orthotopic Living Donor Liver Transplantation With a Small-for-Size Graft for Congenital Absence of the Portal Vein

作者：Matsuura Toshiharu^*; Soejima Yuji; Taguchi Tomoaki

来源：Liver Transplantation, 2010, 16(12): 1437-1439.

DOI：10.1002/lt.22179

Congenital absence of the portal vein (CAPV) with an extrahepatic portosystemic shunt is a rare malformation; the completely absent type, Abernethy malformation type I, is especially rare. Liver transplantation for CAPV type I has been recently recognized as the only curative operation, but few reports have been published so far; meanwhile, auxiliary partial orthotopic liver transplantation (APOLT) has been proposed to be a very effective option, especially for pediatric patients. Here we present an 18-year-old adult patient with CAPV, asplenia, and an iliac shunt vessel who was managed successfully with APOLT using a small-for-size graft. To the best of our knowledge, this is the first adult patient who has experienced success with APOLT for CAPV. This is a feasible procedure: it not only fulfills the metabolic demands of the liver for adult patients but also potentially cures CAPV. Liver Transpl 16:1437-1439, 2010.

• 出版日期2010-12