摘要

Alveolar soft part sarcoma (ASPS) is a rare malignant soft tissue tumor, mainly localized in the extremities, occurring principally in adolescents and young adults. ASPS is uncommon in the female genital tract, and only 37 cases have been reported so far, including 9 cases in the uterine corpus and 17 cases in the uterine cervix. We here reported a case of ASPS occurring in the lower uterine segment. The case showed typical histological and immunohistochemical features. The patient had pelvic and para-aortic lymph node metastasis. To the best of our knowledge, it is the first such case described.