Diphallus with Imperforate Anus and Complete Duplication of Recto-Sigmoid Colon and Lower Urinary Tract

作者：Mirshemirani Alireza^*; Roshanzamir Fatollah; Shayeghi Shahnaz; Mohajerzadeh Leily; Hasas yeganeh Shaghayegh

来源：Iranian Journal of Pediatrics, 2010, 20(2): 229-232.

• Imperforate Anus
• Hindgut duplication
• Double bladder
• Diphallus
• Colo-rectal anomaly

Background: Diphallus is a rare anomaly and accompanying anomalies vary from bifid scrotum, bladder exstrophy, imperforate anus and cob-rectal anomaly such as duplication, and other associated anomalies.
Case Presentation: A 2-day old infant is reported with imperforate anus and complete duplication of recto-sigmoid colon, rectal pouch, doubling of the genitalia with completely formed penis (diphallus), double bladder, urethra and hypospadias. No family history of abnormalities was noted. The patient underwent several operations: laparatory and colostomy at 3rd day of life, and after clinical and paraclinical investigations, cystoplasty, ureteral reimplantation and resection of left phallus were carried out when 4 months old. At the age of 1 year, after colostogram and total colon evaluation, laparatomy, resection of duplicated rectosigmoid colon, and pull-through was carried out; 3 months later colostomy closure was performed and the patient discharged without complications.
Conclusion: The patients with diphallus have to be examined carefully because of the high incidence of other systemic anomalies. Treatment of diphallus usually includes excision of the duplicated penile structure, its urethra, and repair of associated anomalies.

• 出版日期2010-6