Airway management considerations in children with I-cell disease

作者:Mallen Jonathan*; Highstein Mallory; Smith Lee; Cheng Jeffrey
来源:International Journal of Pediatric Otorhinolaryngology, 2015, 79(5): 760-762.
DOI:10.1016/j.ijporl.2015.02.034

摘要

Inclusion-cell disease (mucolipidosis II/I-cell disease) is a lysosomal storage disease characterized by a constellation of physical findings which complicate airway management. There is currently a deficit of published literature describing appropriate strategies for acute management of these children's airways. This paper details emergency and anesthetic airway management concerns and potential solutions in a small series of children with I-cell disease.

  • 出版日期2015-5