A Case of Severe Aortic Valve Regurgitation Caused by an Ascending Aortic Aneurysm in a Young Patient With Autosomal Dominant Polycystic Kidney Disease and Normal Renal Function

作者：Kim Jeongeun; Kim Sang Min; Lee Sang Yeub; Lee Ho Chang; Bae Jang Whan^*; Hwang Kyung Kuk; Kim Dong Woon; Cho Myeong Chan; Byeon Sun Ju; Kim Ki Bong

来源：Korean Circulation Journal, 2012, 42(2): 136-139.

DOI：10.4070/kcj.2012.42.2.136

• Aortic regurgitation
• Aortic aneurysm, thoracic
• Polycystic kidney, autosomal dominant

Aortic aneurysm is one several well-known cardiovascular complications in patients with autosomal dominant polycystic kidney disease (ADPCKD). Commonly affected site of aortic aneurysm and its related dissection in ADPCKD is abdominal aorta. Long standing hypertension, haemodialysis, old age are closely related with discovering of aortic aneurysm and dissection in ADPCKD. However, thoracic aortic aneurysms and its related severe aortic regurgitations (ARs) are rare in younger patients suffering from ADPCKD, especially ones who have normal renal function. Here, we report a case involving a 27-year-old Asian male patient with severe AR due to an ascending aneurysm of the thoracic aorta associated with ADPCKD. The patient had normal renal function without Marfan%26apos;s habitus. The AR and thoracic aortic aneurysm were corrected surgically.

• 出版日期2012-2