Oral findings in Rett syndrome: A systematic review of the dental literature

作者：Fuertes Gonzalez Maria Cristina; Silvestre Francisco Javier^*; Almerich Silla Jose Manuel

来源：Medicina Oral, Patologia Oral y Cirugia Bucal, 2011, 16(1): E37-E41.

DOI：10.4317/medoral.16.e37

• Rett syndrome
• oral manifestations
• bruxism
• review

Rett syndrome (RS) is a chromosome X-linked genetic neurological disorder characterized by developmental regression, particularly in relation to expressive language and use of the hands, together with profound mental retardation, that almost exclusively affects females. The present review describes the 35 cases of RS Publisher in the indexed literature (Medline) - the first corresponding to 1985 and the last to the year 2007. Certain oral manifestations of the disease are derived from the drug treatment prescribed to control the disease, while others are common to other clinical conditions characterized by convulsion activity, difficulties for correct oral hygiene, walking problems and/or an excess of oral/digital-manual habits. In any case, bruxism is the oral habit most frequently associated with RS - the treatment of which remains the subject of controversy.

• 出版日期2011-1