Annuloaortic Ectasia in a Patient With Congenital Absence of the Left Pericardium

作者：Ekeke Chigozirim N; Daniels Curt; Raman Subha V; Hitchcock Charles; Katz Steven E; Crestanello Juan A^*

来源：Annals of Thoracic Surgery, 2013, 96(6): 2243-2245.

DOI：10.1016/j.athoracsur.2013.04.106

We report a patient with congenital absence of the left pericardium with development of progressive annuloaortic ectasia and aortic insufficiency during a 12-year period. The patient was treated with a Bentall procedure. Pathologic examination of the aorta revealed cystic medial necrosis. The surgical management and a possible association between congenital absence of pericardium and Marfan syndrome are discussed.

• 出版日期2013-12