A giant pulmonary artery aneurysm associated with congenital keratoglobus

作者：Alur Ihsan^*; Gunes Tevfik; Pekel Gokhan; Emrecan Bilgin

来源：Turkish Journal of Thoracic and Cardiovascular Surgery, 2016, 24(4): 755-758.

DOI：10.5606/tgkdc.dergisi.2016.13219

• Aneurysm
• aortic root aneurysm
• congenital keratoglobus
• pulmonary artery

Pulmonary artery aneurysms are rare pathologies which may present with Marfan syndrome, EhlerDanlos syndrome, or collagen tissue diseases. These aneurysms may originate from non-congenital causes, such as pulmonary arterial hypertension, tuberculosis, syphilis, candida, mucormycosis, Behcet's disease, giantcell arteritis, or post-trauma vasculitis. The presence of pulmonary artery aneurysm and those of the ascending aorta and aortic root along with a single coronary ostium abnormality accompanied by congenital keratoglobus is a very rare condition. Herein, we present a 33-year-old male with congenital keratoglobus who underwent surgery for a pulmonary artery aneurysm associated with aneurysms of the aorta and aortic root, as well as advanced aortic insufficiency.

• 出版日期2016-10