Multicentric Infantile Hemangiopericytoma: Case Report and Review of the Literature

作者:Sulit Daryl J; Tom Wynnis L; Willert Jennifer R; Nespeca Mark P; Friedlander Sheila Fallon*
来源:Journal of Pediatric Hematology/Oncology, 2011, 33(4): E166-E170.
DOI:10.1097/MPH.0b013e3182145627

摘要

Hemangiopericytomas are rare tumors in which outcome varies with age of onset. Those developing in adults and older children tend to be aggressive with a poor prognosis. However, infantile hemangiopericytomas often behave in a more benign manner. Recent findings suggest aggressive lesions may be histogenetically distinct. Multicentric disease is exceptionally rare, but tends to occur in infants and poses a therapeutic challenge. We present a case with extensive cutaneous and intracranial involvement, which resolved spontaneously. Tumor behavior is a key consideration in management, with careful observation recommended in uncomplicated cases and intervention indicated if more aggressive growth or spread occurs.

  • 出版日期2011-5