Tumefactive multiple sclerosis requiring emergency craniotomy: Case report and literature review

作者:Munarriz Pablo M*; Castano Leon Ana M; Martinez Perez Rafael; Hernandez Lain Aurelio; Ramos Ana; Lagares Alfonso
来源:Neurocirugia, 2013, 24(5): 220-224.
DOI:10.1016/j.neucir.2013.02.008

摘要

Multiple sclerosis (MS) is a demyelinating disease of the central nervous system, characterized by focal neurological dysfunction with a relapsing and remitting course. Tumor-like presentation of MS (or %26quot;tumefactive%26quot;/%26quot;pseudotumoral%26quot; presentation) has been described before with a certain frequency; it consists of a large single plaque (%26gt;2 cm) with presence of edema and mass effect and it is hard to distinguish from a brain tumor. However, we present a very rare case of a 53-year-old woman with a right temporal mass that turned out to be a MS plaque, who deteriorated within hours (brain herniation with loss of consciousness and unilateral mydriasis) and required an emergency craniotomy. We also present a review of the literature. It appears that only 4 cases of emergency craniotomy/craniectomy required in a patient with a tumor-like MS plaque have been reported before.

  • 出版日期2013-10