Bilateral submandibular gland oncocytoma in a patient with multiple endocrine neoplasia 2B syndrome and neurofibromatosis type 1: an unusual case

作者：Dastaran Mehrnoosh; Chandu Arun^*

来源：International Journal of Oral and Maxillofacial Surgery, 2011, 40(7): 764-767.

DOI：10.1016/j.ijom.2011.02.017

• oncocytoma
• monomorphic adenoma
• submandibular gland
• salivary
• neurofibromatosis
• multiple endocrine neoplasia syndrome

Oncocytomas are unusual neoplasms of the head and neck that occur mainly in the parotid gland. The authors report a case of bilateral submandibular gland oncocytoma in a patient with multiple endocrine neoplasia 2B syndrome and neurofibromatosis type 1. Histopathology of the resection specimens demonstrated lymphovascular invasion but no other aggressive features. This was a highly unusual feature in an otherwise rare benign tumour.

• 出版日期2011-7