Adrenocorticotropic hormone-producing pheochromocytoma: a case report and review of the literature

作者：Li Xun-gang; Zhang Dong-xu; Li Xiang; Cui Xin-gang^*; Xu Dan-feng; Li Yao; Gao Yi; Yin Lei; Ren Ji-zhong

来源：Chinese Medical Journal, 2012, 125(6): 1193-1196.

DOI：10.3760/cma.j.issn.0366-6999.2012.06.042

• adrenocorticotropic hormone syndrome
• Cushing's syndrome
• ectopic
• laparoscopy
• pheochromocytoma

Ectopic Cushing's syndrome caused by pheochromocytoma is rare: We reported a 15-year-old female patient who was admitted to hospital with typical Cushing's syndrome. She had not started menstruation. Her plasma adrenocorticotropic hormone (ACTH) and 24-hour urinary free cortisol levels were extremely high. Gonadal and progestational hormone levels were also abnormal. Abdominal computed tomography scans and enhanced scans revealed multiple irregular tumors in the right adrenal. Pelvic echogram showed an infantile uterus, while the ovaries were at an immature stage of development. Retroperitoneal laparoscopic right adrenalectomy was performed without intraoperative complications. Histology and immunohistochemistry of the tumor were consistent with pheochromocytoma. Retroperitoneal laparoscopic adrenalectomy is a safe procedure with satisfactory outcomes and allows for rapid recovery. Chin Med J 2012;125(6):1193-1196

• 出版日期2012-3-20
• 单位天津市中医药研究院附属医院; 中国人民解放军第二军医大学