Adult presentation of spinal dysraphism and tandem diastematomyelia

作者：Porensky Paul^*; Muro Kenji; Ganju Aruna

来源：Spine Journal, 2007, 7(5): 622-626.

DOI：10.1016/j.spinee.2006.08.006

• diastematomyelia
• type I split-cord malformation
• scoliosis
• tethered cord
• adult presentation
• intradural extramedullary epidermoid tumor

BACKGROUND CONTEXT: Diasternatomyelia is a split-cord malformation often accompanied by other cord or column anomalies.
PURPOSE: To report on an adult patient with diastematomyelia and discuss the embryological basis and related developmental sequelae of this split-cord malformation.
STUDY DESIGN: Case report.
METHODS: A summary of the management of a 54-year-old woman with recent clinical symptomatology related to an undiagnosed split-cord malformation is presented with accompanying literature review.
RESULTS: A rare adult presentation of diastematomyelia with accompanying intradural extramedullary epidermoid tumor was repaired with resection of the soft-tissue mass and excision of the fibro-osseous septum.
CONCLUSION: Initial presentation of diastematomyelia is rarely seen in adults; accompanying pathology includes scoliosis, tethered cord, and intradural tumors. Effective treatment involves identification of the primary pathology.

• 出版日期2007-10
• 单位西北大学