Anesthesia management of a ganglioneuroma with seizures presenting as pheochromocytoma

作者：Batra Yatindra Kumar^*; Rajeev Subramanyam; Rao Katragadda L N

来源：Paediatric Anaesthesia, 2007, 17(5): 479-483.

DOI：10.1111/j.1460-9592.2006.02143.x

• anesthesia
• ganglioneuroma
• seizures
• child
• pheochromocytoma

Ganglioneuromas (GN) are neural crest cell-derived tumors which may coexist with pheochromocytomas, secrete various neuropeptides or the symptoms may mimic that of a pheochromocytoma, producing hypertension or a hypotensive crisis during anesthesia for these tumors. We report here the case of a 7-year-old female child with an adrenal tumor suspected to be a pheochromocytoma, later confirmed by histology as a GN. This child presented with episodic headache, anxiety, palpitations and 3D helical (spiral) computed tomography of the abdomen revealed an adrenal tumor. In addition, the child was diagnosed to have a seizure disorder. She was managed as a pheochromocytoma. Although the child's preoperative catecholamine levels were normal, tumor manipulation caused a hypertensive crisis. We discuss the clinical characteristics of this unusual case, anesthesia management, and the postoperative course.

• 出版日期2007-5
• 单位河北医科大学