An autopsy case of refractory vasculo-Behcet's disease

作者:Kaieda Shinjiro*; Zaizen Yoshiaki; Nomura Yoriko; Okabe Koki; Honda Seiyo; Kage Masayoshi; Ida Hiroaki; Hoshino Tomoaki; Fukuda Takaaki
来源:Modern Rheumatology, 2015, 25(2): 307-311.
DOI:10.3109/14397595.2013.874755

摘要

Pulmonary vascular involvement in Behcet's disease is a rare complication with a poor prognosis. We present an autopsy case of vasculo-Behcet's disease complicated by pulmonary hemorrhage, possibly caused by rupture of pulmonary artery aneurysms. The patient was treated with a combination of high-dose steroids and pulse cyclophosphamide, but he died from massive hemoptysis. This case highlights the need for potent new therapies for patients with vasculo-Behcet's disease refractory to conventional immunosuppressive therapy, such as a combination of steroids and cyclophosphamide.

  • 出版日期2015-3