Doege-potter syndrome: a report of a histologically benign but clinically malignant case

作者：Kim Do Wan; Na Kook Joo; Yun Ju Sik; Song Sang Yun^*

来源：Journal of Cardiothoracic Surgery, 2017, 12(1): 64.

DOI：10.1186/s13019-017-0630-4

• Pleural disease
• Tumor
• Benign
• Fibrous neoplasm

Background: Solitary fibrous tumors of the pleura (SFTPs) are relatively rare tumors that originate from mesenchymal cells of submesothelial tissue of the pleura. Most patients with SFTPs are asymptomatic; however, pleuritic chest pain, cough, and dyspnea can develop. If hypoglycemia is associated with a solitary fibrous tumor, it is referred to as the Doege-Potter syndrome.
Case presentation: A 70-year-old man had visited our hospital with a chief complaint of dyspnea, and he was diagnosed as having a solitary fibrous tumor. A few years later, he developed hypoglycemia, and he underwent excision of the mass.
Conclusion: Occasionally, SFTPs induce several paraneoplastic events, such as hypertrophic osteoarthropathy. We described here a patient with an SFTP with Doege-Potter syndrome who was successfully treated with complete resection. Although lesions can be histologically benign, they can clinically present with malignant features.

• 出版日期2017-8-7