摘要

Atypical teratoid/rhabdoid tumours (AT/RT) are aggressive neoplasms of the central nervous system occurring mainly in the paediatric population. We reported a 32-year-old male patient who was admitted in emergency in unconscious state. The neoplasm was localised in the left frontal region and was totally excised. The histological and immunohistochemical report revealed AT/RT. This unusual presentation underlines the necessity of considering this devastating neoplasm in the differential diagnosis of malignant brain tumours of adults.