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ALS mutations in FUS cause neuronal dysfunction and death in Caenorhabditis elegans by a dominant gain-of-function mechanism
ALS herbicide resistance mutations in Raphanus raphanistrum: evaluation of pleiotropic effects on vegetative growth and ALS activity
ALS and Oxidative Stress: The Neurovascular Scenario
ALS Multicenter Cohort Study of Oxidative Stress (ALS COSMOS): Study methodology, recruitment, and baseline demographic and disease characteristics
ALS pathophysiology: Insights from the split-hand phenomenon
ALS and FTD: two sides of the same coin?
ALS dysphagia pathophysiology Differential botulinum toxin response
ALS mutant FUS disrupts nuclear localization and sequesters wild-type FUS within cytoplasmic stress granules
ALS and neuromuscular disease: in search of the Holy Grail
ALS model-based comparison of Cosmo-SkyMed and TerraSAR-X HS DSMs on varied land forms
ALS mutations in TLS/FUS disrupt target gene expression
ALS spinal neurons show varied and reduced mtDNA gene copy numbers and increased mtDNA gene deletions
ALS disease onset may occur later in patients with pre-morbid diabetes mellitus
ALS mutant SOD1 interacts with G3BP1 and affects stress granule dynamics
ALS Mutations Disrupt Phase Separation Mediated by alpha-Helical Structure in the TDP-43 Low-Complexity C-Terminal Domain
ALS disrupts spinal motor neuron maturation and aging pathways within gene co-expression networks
ALS and physician-assisted suicide
ALS and Frontotemporal Dementia - Case Report and Review of the Literature
ALS genetic modifiers that increase survival of SOD1 mice and are suitable for therapeutic development
ALS pathogenesis: Recent insights from genetics and mouse models
ALS precursor finally shaken into fibrils
ALS patients with mutations in the SOD1 gene have an unique metabolomic profile in the cerebrospinal fluid compared with ALS patients without mutations
ALS Untangled No. 20: The Deanna Protocol
ALS Along the Axons - Expression of Coding and Noncoding RNA Differs in Axons of ALS models
ALS Pathogenesis and Therapeutic Approaches: The Role of Mesenchymal Stem Cells and Extracellular Vesicles
ALS mutant FUS proteins are recruited into stress granules in induced pluripotent stem cell-derived motoneurons
ALS and FTD linked GGGGCC-repeat containing DNA oligonucleotide folds into two distinct G-quadruplexes
ALS and frontotemporal dementia belong to a common disease spectrum
ALS treatment: State of the art in 2014 and perspectives
ALS patients with SOD1 mutations in Switzerland show very diverse phenotypes and extremely long survival
ALS Associated Mutations in Matrin 3 Alter Protein-Protein Interactions and Impede mRNA Nuclear Export
ALS clinical trials Do enrolled patients accurately represent the ALS population?
ALS RISK BUT NOT PHENOTYPE IS AFFECTED BY ATAXIN-2 INTERMEDIATE LENGTH POLYGLUTAMINE EXPANSION
ALS and FTD: an epigenetic perspective
ALS Patient Stem Cells for Unveiling Disease Signatures of Motoneuron Susceptibility: Perspectives on the Deadly Mitochondria, ER Stress and Calcium Triad
ALS mouse model SOD1(G93A) displays early pathology of sensory small fibers associated to accumulation of a neurotoxic splice variant of peripherin
ALS Clinical Trials Review: 20 Years of Failure. Are We Any Closer to Registering a New Treatment?
ALS Genes in the Genomic Era and their Implications for FTD
ALS genosensing using DNA-hybridization electrochemical biosensor based on label-free immobilization of ssDNA on Sm2O3 NPs-rGO/PANI composite
ALS, cognition and the clinic
ALS-associated mutation FUS-R521C causes DNA damage and RNA splicing defects
ALS-associated peripherin spliced transcripts form distinct protein inclusions that are neuroprotective against oxidative stress
ALS-Plus - Where does it begin, where does it end?
ALS-Plus syndrome: Non-pyramidal features in a large ALS cohort
ALS-Associated TDP-43 Induces Endoplasmic Reticulum Stress, Which Drives Cytoplasmic TDP-43 Accumulation and Stress Granule Formation
ALS-Linked Mutations Enlarge TDP-43-Enriched Neuronal RNA Granules in the Dendritic Arbor
ALS-associated mutations in FUS disrupt the axonal distribution and function of SMN
ALS-FTD Complex Disorder due to C9ORF72 Gene Mutation: Description of First Polish Family
ALS-linked TDP-43 mutations produce aberrant RNA splicing and adult-onset motor neuron disease without aggregation or loss of nuclear TDP-43
ALS-associated protein FIG4 is localized in Pick and Lewy bodies, and also neuronal nuclear inclusions, in polyglutamine and intranuclear inclusion body diseases
ALS-causing P56S mutation and splicing variation on the hVAPB MSP domain transform its beta-sandwich fold into lipid-interacting helical conformations
ALS-Associated FUS Mutations Result in Compromised FUS Alternative Splicing and Autoregulation
ALS-Causing Mutations Significantly Perturb the Self-Assembly and Interaction with Nucleic Acid of the Intrinsically Disordered Prion-Like Domain of TDP-43
ALS-associated mutant FUS induces selective motor neuron degeneration through toxic gain of function
ALS-Resistant Annual Sedge (Cyperus compressus) Confirmed in Turfgrass
ALS-008176 for Respiratory Syncytial Virus Infection
ALS-Resistant Smallflower Umbrella Sedge (Cyperus difformis) in Arkansas Rice: Physiological and Molecular Basis of Resistance
ALS-causative mutations in FUS/TLS confer gain and loss of function by altered association with SMN and U1-snRNP
ALS-associated P56S-VAPB mutation restrains 3T3-L1 preadipocyte differentiation
ALS-Linked P56S-VAPB Mutation Impairs the Formation of Multinuclear Myotube in C2C12 Cells
ALS-linked mutant superoxide dismutase 1 (SOD1) alters mitochondrial protein composition and decreases protein import
ALS-associated mutations in TDP-43 increase its stability and promote TDP-43 complexes with FUS/TLS
ALS-associated fused in sarcoma (FUS) mutations disrupt Transportin-mediated nuclear import
ALS-linked mutant SOD1 damages mitochondria by promoting conformational changes in Bcl-2
ALS-linked protein disulfide isomerase variants cause motor dysfunction
ALS-FTLD associated mutations of SQSTM1 impact on Keap1-Nrf2 signalling
ALS-Resistant Spotted Spurge (Chamaesyce maculata)n Confirmed in Georgia
ALS-Associated Ataxin 2 PolyQ Expansions Enhance Stress-Induced Caspase 3 Activation and Increase TDP-43 Pathological Modifications
ALS-IgG-induced selective motor neurone apoptosis in rat mixed primary spinal cord cultures
ALS-related misfolded protein management in motor neurons and muscle cells
ALS-linked P56S-VAPB, an aggregated loss-of-function mutant of VAPB, predisposes motor neurons to ER stress-related death by inducing aggregation of co-expressed wild-type VAPB
ALS-Causing SOD1 Mutations Promote Production of Copper-Deficient Misfolded Species
ALS-dying forward, backward or outward?
ALS-causing cleavages of TDP-43 abolish its RRM2 structure and unlock CTD for enhanced aggregation and toxicity
ALS-causing mutations differentially affect PGC-1 alpha expression and function in the brain vs. peripheral tissues
ALS-linked mutant SOD1 proteins promote A beta aggregates in ALS through direct interaction with A beta
ALS-causing profilin-1-mutant forms a non-native helical structure in membrane environments
ALS-FUS pathology revisited: singleton FUS mutations and an unusual case with both a FUS and TARDBP mutation
ALS-Associated Endoplasmic Reticulum Proteins in Denervated Skeletal Muscle: Implications for Motor Neuron Disease Pathology
ALS-linked misfolded SOD1 species have divergent impacts on mitochondria
ALS-based estimation of plot volume and site index in a eucalyptus plantation with a nonlinear mixed-effect model that accounts for the clone effect
ALS-008176 for Respiratory Syncytial Virus Infection REPLY
ALS-associated mutation SOD1(G93A) leads to abnormal mitochondrial dynamics in osteocytes